Ischemic priapism in sickle cell disease as a cause of sexual dysfunction. Case series and literature review

Priapismo isquémico en la enfermedad falciforme como causa de disfunción sexual. Serie de casos y revisión de la literatura

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Español
Rita Magola Sierra Merlano
Keyner Toro Osorio
Abstract

Sickle cell disease (SCD) comprises a group of hereditary disorders with heterogeneous clinical expression and multiple complications of a vascular and hemolytic nature. Priapism represents a urological emergency that requires early surgical intervention to reduce erectile dysfunction. Objectives: Report five cases of SCD treated for priapism at the ESE University Hospital of Cartagena (ESEHUC), and highlight the sociodemographic, clinical and laboratory characteristics that were associated with erectile dysfunction. Methods: Hospital case series. Results: Five cases of priapism were recorded with a median calculated for age of 33 years, BMI: 23 kg/m2, three cases belonged to the homozygous subtype, one double heterozygous, and one sickle cell trait. The average hospital admission was considered late, being greater than 48 hours of evolution of priapism and urological surgical management was chosen in all of them. Three cases presented sexual dysfunction, one was classified as severe. Conclusions: Cases with subclinical forms and low-risk genotypes may face greater priapism, with a risk of complications with an impact on sexual life. We insist on educating patients about: early consultation, and lifestyles that reduce the risk of priapism.

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Author Biographies (SEE)

Español, Universidad de Cartagena, Facultad de Medicina. Cartagena, Colombia

Médico. Especialista en Medicina Interna.

Rita Magola Sierra Merlano, Español

Médica. Especialista en Medicina Interna y Reumatología. PhD Ciencias de la Educación. 

Keyner Toro Osorio, Español

Médico. Especialista en Medicina Interna y Vascular.

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