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Sindrome de Kasabach-Merritt, una patología rara y potencialmente mortal en pediatría

Sindrome de Kasabach-Merritt, una patología rara y potencialmente mortal en pediatría



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Paz Amador KJ, Jaimes Hernández LX. Sindrome de Kasabach-Merritt, una patología rara y potencialmente mortal en pediatría. Rev. colomb. hematol. oncol. [Internet]. 2023 Jun. 28 [cited 2025 Dec. 6];9(2-Supl):275-8. https://doi.org/10.51643/22562915.605

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Hemato-oncología Pediátrica

How to Cite
1.
Paz Amador KJ, Jaimes Hernández LX. Sindrome de Kasabach-Merritt, una patología rara y potencialmente mortal en pediatría. Rev. colomb. hematol. oncol. [Internet]. 2023 Jun. 28 [cited 2025 Dec. 6];9(2-Supl):275-8. https://doi.org/10.51643/22562915.605

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Kelly Johana Paz Amador
    Laura Ximena Jaimes Hernández

      Abstract: A clinical case of a Kasabach-Merritt syndrome secondary to a kaposiform hemangioendothelioma in a 2-month-old child is presented, which was confirmed clinically, laboratory tests and magnetic resonance imaging. The expression of the disease was characterized by a rapidly growing vascular tumor on the left thigh that progressed to disseminated intravascular coagulation that was difficult to control, requiring multiple transfusions and pharmacological support to compensate for its life-threatening condition.


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